Prune Belly syndrome; a complex congenital anomaly of 10 cases from a tertiary hospital

damte shimelis awoke | Bio
Addis Ababa University
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  • Submited: March 11, 2020
  • Published: December 31, 2020

Abstract

Background: is a rare congenital multisystemic disorder characterized by absence of abdominal wall muscles, dilated urinary bladder, a variety of other urologic abnormalities and undescended testes in males. Patients could have additional pulmonary hypoplasia, a variety of cardiac abnormalities and kyphoscoliosis. Here we present 10 pediatric patients who were on follow up at our renal clinic of the Department of Pediatrics and Child Health of Tikur Anbessa Specialized Teaching Hospital.

 

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How to Cite
awoke, damte shimelis. (2020). Prune Belly syndrome; a complex congenital anomaly of 10 cases from a tertiary hospital. Ethiopian Medical Journal, 59(01). Retrieved from https://www.emjema.org/index.php/EMJ/article/view/1506

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